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UBA1 and ECHS1
Number of citations of the paper that reports this interaction (PubMedID
21988832
)
38
Data Source:
BioGRID
(two hybrid)
UBA1
ECHS1
Description
ubiquitin like modifier activating enzyme 1
enoyl-CoA hydratase, short chain 1
Image
GO Annotations
Cellular Component
Heterochromatin
Nucleus
Nucleoplasm
Cytoplasm
Mitochondrion
Lysosomal Membrane
Cytosol
Endosome Membrane
Desmosome
Rough Endoplasmic Reticulum Membrane
Extracellular Exosome
Mitochondrion
Mitochondrial Matrix
Molecular Function
Nucleotide Binding
RNA Binding
Ubiquitin Activating Enzyme Activity
Protein Binding
ATP Binding
Ubiquitin-like Modifier Activating Enzyme Activity
Ligase Activity
Catalytic Activity
Delta(3)-delta(2)-enoyl-CoA Isomerase Activity
Enoyl-CoA Hydratase Activity
Protein Binding
Lyase Activity
Isomerase Activity
3-hydroxyacyl-CoA Dehydratase Activity
3-hydroxypropionyl-CoA Dehydratase Activity
Crotonyl-CoA Hydratase Activity
Biological Process
Ubiquitin-dependent Protein Catabolic Process
DNA Damage Response
Protein Ubiquitination
Lipid Metabolic Process
Fatty Acid Metabolic Process
Fatty Acid Beta-oxidation
Branched-chain Amino Acid Catabolic Process
Pathways
Synthesis of active ubiquitin: roles of E1 and E2 enzymes
Antigen processing: Ubiquitination & Proteasome degradation
Branched-chain amino acid catabolism
Beta oxidation of lauroyl-CoA to decanoyl-CoA-CoA
Beta oxidation of decanoyl-CoA to octanoyl-CoA-CoA
Beta oxidation of octanoyl-CoA to hexanoyl-CoA
Beta oxidation of hexanoyl-CoA to butanoyl-CoA
Beta oxidation of butanoyl-CoA to acetyl-CoA
Mitochondrial short-chain enoyl-CoA hydratase deficiency 1
Drugs
Hexatantalum Dodecabromide
Quercetin
Hexanoyl-CoA
Octanoyl-Coenzyme A
Acetoacetyl-CoA
4-(N,N-Dimethylamino)cinnamoyl-CoA
Omega-3-carboxylic acids
Diseases
Spinal muscular atrophy (SMA), including: SMA type I (SMA1) / Werdning-Hoffman disease; SMA type II (SMA2); SMA type III (SMA3) / Kugeleberg-Welander disease; SMA type IV (SMA4); X-linked SMA 2 (SMAX2); X-linked distal SMA 3 (DSMAX); Distal SMA autosomal recessive type 4 (DSMA4); Congenital distal spinal muscular atrophy (SMAL); SMA proximal adult autosomal dominant (SMAPAD)
GWAS
Lifespan (
25918517
)
Nonunion in individuals with fractures (
30680360
)
Serum metabolite levels (
33031748
)
Interacting Genes
51 interacting genes:
ABCF1
AZGP1P2
BUB3
CDK1
CEBPA
CHEK1
ECHS1
GAN
GRB2
HGS
HSPH1
LINC01554
MGMT
MTNR1A
OGT
PIAS3
SEMA3F
SMAD5
SUMO2
TAF9
TMCC2
TSSC4
TTC19
UBC
UBE2A
UBE2B
UBE2C
UBE2D1
UBE2D2
UBE2D3
UBE2D4
UBE2E1
UBE2E2
UBE2E3
UBE2G1
UBE2J1
UBE2J2
UBE2K
UBE2L1
UBE2L3
UBE2L6
UBE2M
UBE2N
UBE2Q2
UBE2R2
UBE2S
UBE2T
UBE2U
UBE2W
UBE2Z
UBTD2
16 interacting genes:
CAPN1
CDC42
CLDN12
CYP2E1
ERCC6
FXR1
FXR2
GRB2
KAT2A
LRRK1
LRRK2
PPM1B
SERPINA1
SIRT3
UBA1
ZNG1B
Entrez ID
7317
1892
HPRD ID
02440
03799
Ensembl ID
ENSG00000130985
ENSG00000127884
Uniprot IDs
A0A024R1A3
P22314
P30084
PDB IDs
4P22
6DC6
7PYV
2HW5
Enriched GO Terms of Interacting Partners
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Ubiquitin Conjugating Enzyme Activity
Protein Polyubiquitination
Protein Modification By Small Protein Conjugation
Post-translational Protein Modification
Ubiquitin-protein Transferase Activity
Protein Ubiquitination
Protein K48-linked Ubiquitination
Ubiquitin-like Protein Transferase Activity
Protein Modification Process
Protein K11-linked Ubiquitination
Modification-dependent Protein Catabolic Process
Proteolysis Involved In Protein Catabolic Process
ATP Binding
Transferase Activity
Ubiquitin-dependent Protein Catabolic Process
Nucleotide Binding
Protein Metabolic Process
Macromolecule Catabolic Process
Proteolysis
Ubiquitin Protein Ligase Binding
Protein Monoubiquitination
Macromolecule Metabolic Process
Catabolic Process
Protein K63-linked Ubiquitination
Proteasomal Protein Catabolic Process
Protein K6-linked Ubiquitination
Proteasome-mediated Ubiquitin-dependent Protein Catabolic Process
Protein Catabolic Process
Nucleoplasm
ISG15 Transferase Activity
HULC Complex
DNA Damage Response
ISG15-protein Conjugation
Regulation Of Post-translational Protein Modification
Free Ubiquitin Chain Polymerization
Nucleus
DNA Repair
Positive Regulation Of Post-translational Protein Modification
Protein K29-linked Ubiquitination
Cellular Response To Stress
Cell Cycle Phase Transition
Ubiquitin Binding
Regulation Of Protein Modification Process
Protein K27-linked Ubiquitination
Positive Regulation Of Protein Ubiquitination
Ubiquitin Ligase Complex
Positive Regulation Of Protein Metabolic Process
Regulation Of Protein Ubiquitination
TORC1 Signaling
DNA Metabolic Process
Regulation Of Translation At Presynapse, Modulating Synaptic Transmission
Intracellular Distribution Of Mitochondria
Positive Regulation Of Long-term Neuronal Synaptic Plasticity
Postsynapse
Cytoplasmic Ribonucleoprotein Granule
Mitochondrion Distribution
Positive Regulation Of Canonical Wnt Signaling Pathway
Translation Regulator Activity
Neuron Projection
Regulation Of Reactive Oxygen Species Metabolic Process
Dentate Gyrus Development
Regulation Of Long-term Neuronal Synaptic Plasticity
GTP Binding
Positive Regulation Of Wnt Signaling Pathway
Identical Protein Binding
Carbon Tetrachloride Metabolic Process
Halogenated Hydrocarbon Metabolic Process
4-nitrophenol Metabolic Process
4-nitrophenol 2-monooxygenase Activity
Benzene Metabolic Process
Regulation Of Defense Response
Regulation Of Synaptic Plasticity
Acyltransferase Activity, Transferring Groups Other Than Amino-acyl Groups
Peptidyl-lysine Glutarylation
Histone Glutaryltransferase Activity
Histone Succinyltransferase Activity
Modulation Of Chemical Synaptic Transmission
Peptide Glutaryltransferase Activity
Guanyl-nucleotide Exchange Factor Adaptor Activity
Presynaptic Modulation Of Chemical Synaptic Transmission
Positive Regulation Of Catalase Activity
Positive Regulation Of Superoxide Dismutase Activity
Cellular Response To Curcumin
Caveola Neck
GTP-dependent Protein Kinase Activity
Wnt Signalosome Assembly
Mitochondrion Localization
Regulation Of Cell Communication
Small GTPase-mediated Signal Transduction
Regulation Of Intracellular Signal Transduction
GBD Domain Binding
Storage Vacuole
Regulation Of Signaling
Regulation Of Defense Response To Virus
JNK Cascade
Positive Regulation Of Peptidyl-serine Phosphorylation Of STAT Protein
Histone H3K9 Acetyltransferase Activity
Grb2-EGFR Complex
Regulation Of Canonical Wnt Signaling Pathway
Regulation Of Neuronal Synaptic Plasticity
Tagcloud
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Tagcloud (Difference)
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Tagcloud (Intersection)
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